Coexistence of two types of clinical lesions in childhood-onset mastocytosis

Simple item page
dc.contributor.authorPérez-Pérez, Lidiaen_US
dc.contributor.authorAllegue, Franciscoen_US
dc.contributor.authorCaeiro, José Luisen_US
dc.contributor.authorFabeiro, José Maríaen_US
dc.contributor.authorRodríguez, Alberto Pérezen_US
dc.contributor.authorZulaica, Anderen_US
dc.date.accessioned2014-05-06T22:32:02Z
dc.date.available2014-05-06T22:32:02Z
dc.date.issued2011-10-06en_US
dc.descriptionThe vast majority of mastocytosis appear in childhood, urticaria pigmentosa (UP) and mastocytomas being the most common types. Terms such as "xanthelasmoid mastocytosis", "pseudoxanthomatous mastocytosis" or "nodular mastocytosis" have been introduced in the literature to describe the presence of yellowish papular or nodular lesions. We describe two children with cutaneous mastocytosis showing yellowish lesions in combination with other skin lesions. A 10-year-old girl presented with asymptomatic lesions in her vulva at birth, and developed brownish macules on her trunk years after. An eight- year-old boy presented with multiple yellowish papular lesions on his trunk, neck and limbs coexisting with a few clinically anetodermic lesions. No systemic involvement was found and the skin biopsy confirmed a cutaneous mastocytosis in both cases. The two patients are currently asymptomatic and are being periodically followed up. Mastocytoses may show a variety of clinical lesions, sometimes leading to misdiagnosis. Although there are previous reports, involvement of the mucosae and secondary anetoderma are not common findings in cutaneous mastocytoses. We consider that cutaneous manifestations of mastocytoses compose a clinical spectrum, thus explaining the coexistence of different clinical lesions and the development of uncommon presentations.en_US
dc.identifier.urihttp://hdl.handle.net/1807/48812
dc.identifier.urihttp://www.bioline.org.br/abstract?id=dv11050en_US
dc.identifier.urihttp://www.bioline.org.br/dven_US
dc.identifier.urihttp://www.ijdvl.comen_US
dc.languageenen_US
dc.locationOrigin of publication: Indiaen_US
dc.publication.journalIndian Journal of Dermatology, Venereology and Leprology (ISSN: 0378-6323) Vol 77 Num 2en_US
dc.publisherMedknow Publications on behalf of The Indian Association of Dermatologists, Venereologists and Leprologists (IADVL)en_US
dc.rights.holderCopyright 2011 Indian Journal of Dermatology, Venereology, and Leprology.en_US
dc.subjectanetodermaen_US
dc.subjectxanthelasmoid mastocytosisen_US
dc.subjectpseudoxanthomatous mastocytosisen_US
dc.subjectNodular mastocytosisen_US
dc.titleCoexistence of two types of clinical lesions in childhood-onset mastocytosisen_US
dc.typeArticleen_US

Files

Original bundle

Now showing 1 - 1 of 1
Thumbnail Image
Name:
dv11050.html
Size:
41.91 KB
Format:
Hypertext Markup Language
Download

Collections

Indian Journal of Dermatology, Venereology and Leprology